The link is not 100% but two hunters eating from the same deer population and falling ill at around the same time is extremely unlikely to be a coincidence.
We are essentially one mutation away from this spreading between humans and that would be very, very bad.
True that it's not a virus but prions can mutate in the sense that they are just proteins like any other, produced according to their genes. The gene coding for the prion protein can mutate, producing a prion that is better at making, e.g., the human analog fold into a prion.
They aren't produced according the their genes. They don't affect DNA like viruses do. They are a removed lower energy configuration of a protein. When the removed protein bumps into a healthy form of itself, the forces between the molecules pull the healthy protein into the prion shape. Then they go their separate ways, exponentially eating holes through tissues.
The protein targeted by CWD is different in cervids, it has like an extra loop that is important for its function. So if a CWD prion bumps into the human version of the protein, nothing happens. But, if some weird interaction allowed it to actually work, it's feasible a human prion could be created.
Prions are the best candidate IMO for a near-to-medium-term human extinction event. If a bad one gets a foothold then median human life expectancy will be like 12 years within a century or two and there'll be nothing to be done about it
You should probably be scareder of CWD and similar diseases TBQH IMHO PBJ
It's everywhere by now, isn't it? When the containment of a new disease is precarious like this, I usually assume the worst has already happened. The people in charge just aren't aware of it yet. If they are, they still don't want to tell the public out of fear of how destabilizing such news could be to the whole system.
The maps of affected wild herds only shows a few states, but I've seen deer here in NJ as far back as a decade ago that very much looked like they were sick with CWD. I wouldn't doubt that it's more widespread than we are aware of.
With so many possibilities of deer and cattle coming into contact in rural settings, I especially worry about my relatives that have cattle and occasionally hunt. I guess my mother had a point about never wanting to try any venison that they cooked.
It's a certain protein that got misfolded, if it comes in contact with more of the original protein it causes that to also get misfolded. It can spread kinda similarly to a virus, via bodily fluids, animal-animal contact, in contaminated food/water, and by eating tainted meat in this case. Even if the deer was asymptomatic they can still spread the disease. The way the protein is folded causes it to be resistant to degradation so it can lay dormant for years or maybe decades in the environment. It causes horrifying symptoms causing deer to almost turn into zombies as their bodies waste away.
If anything this just shows how cowardly hunters are. Who tf shoots a clearly diseased animal and then takes it home acting like they shot it on their own merits?
If the poor thing's visibly suffering from CWD, it absolutely is not good meat. When I was living in the sticks, I didn't know a single subsistence hunter who'd eat a visibly-diseased buck-- the sport hunters might've still gone after them, but I don't tolerate sport hunters in my physical locality, so I don't talk to them.
CWD is a prion disease. If a human died from a prion disease it would be very easy to detect and the symptoms would be obvious
Always get your venison tested for CWD but I want more than a speculative barstool sports tweet to confirm we have a new Creutzfeldt Jakob disease on our hands